Abstract

Klippel-Trenanay Syndrome (KTS) consists of a triad of cutaneous haemangioma, bone and soft tissue hypertrophy and venous varicosities (4). The aetiology of this syndrome is unknown but some authors have suggested that it results from a mesodermal abnormality that occurs during fetal development (5). Bone hypertrophy usually results in limb length discrepancy, with the affected leg being the longer one. In most of the patients with limb length discrepancy due to KTS, operative treatment of the affected leg takes place before skeletal maturity.